Produzem um shunt direita-esquerda 6. Reservam-se a Dermosseptoplastia e os retalhos locais e microvasculares para os quadros mais graves Rev Bras Otorrinolaringol ; Hereditary haemorrhagic telangiectasia Osler-Weber-Rendu syndrome : otorhinolaryngological manifestation. Clin Otolaryngol ; Hereditary Haemorragic Telangiectasia.
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Produzem um shunt direita-esquerda 6. Reservam-se a Dermosseptoplastia e os retalhos locais e microvasculares para os quadros mais graves Rev Bras Otorrinolaringol ; Hereditary haemorrhagic telangiectasia Osler-Weber-Rendu syndrome : otorhinolaryngological manifestation. Clin Otolaryngol ; Hereditary Haemorragic Telangiectasia. New England J Med ; Arch Intern Med ;56 8 Genetic epidemiolology oh Hereditary hemorragic telangiectasia in a local communityin the northern part of Japan.
Clinical and molecular genetic features of Pulmonary Hypertension in patients with Hereditary Hemorrhagic Telangiectasia. N Engl J Med ; 5 Hereditary Hemorragic Telangiectasia Osler Weber Disease - An electron microscopic study of the vascular lesions before and after therapy with hormones.
Arch Otolaryngol ; Ultrastructure and three-dimensional organization of the telangiectases of hereditary hemorrhagic telangiectasia. J Invest Dermatol ; Perry WH. Am J Medicine ; Hereditary haemorragic telangiectasia Osler-WeberRendu syndrome : otorhinolaringological manifestations. Clin Otolaryngol ;26 2 Liver disease in patients with hereditary hemorrhagic telangiectasia.
N Engl J Med ; 13 Arquivos de Otorrinolaringologia ; Control of epistaxis in patients with Herditary Hemorragic Telangiectasia. Otol Head Neck Surg ; Closure of nasal cavities in the treatment of refractory Hereditary Haemorrhagic Telangiectasia. J Laryngol Otol ; Epistaxis in Rendu-Weber-Osler Disease.
The role of Brachytherapy. Acta Otorhinolaryngol Ita ; Artigo aceito em 13 de setembro de Disciplina de Otorrinolaringologia. All the contents of this journal, except where otherwise noted, is licensed under a Creative Commons Attribution License. Services on Demand Journal. How to cite this article.
2016, Número 6
Hereditary hemorrhagic telangiectasia HHT , also known as Osler—Weber—Rendu disease and Osler—Weber—Rendu syndrome , is a rare autosomal dominant genetic disorder that leads to abnormal blood vessel formation in the skin , mucous membranes , and often in organs such as the lungs , liver , and brain. It may lead to nosebleeds , acute and chronic digestive tract bleeding , and various problems due to the involvement of other organs. Treatment focuses on reducing bleeding from blood vessel lesions, and sometimes surgery or other targeted interventions to remove arteriovenous malformations in organs. Chronic bleeding often requires iron supplements and sometimes blood transfusions. HHT is transmitted in an autosomal dominant fashion, and occurs in one in 5,—8, people in North America. Telangiectasia small vascular malformations may occur in the skin and mucosal linings of the nose and gastrointestinal tract.
Hereditary hemorrhagic telangiectasia
Colour-Doppler features of hepatic involvement in Rendu-Osler-Weber disease. Department of Digestive Diseases. Hospital Universitario Virgen de la Arrixaca. Murcia, Spain. A year-old woman with a past history of Rendu-Osler-Weber disease of 16 years was referred to our unit to evaluate hepatic involvement. Previous pulmonary arteriovenous malformations were treated with embolization.